Brown syndrome associated with Marcus-Gunn jaw winking ptosis

Ilaria Biagini, Alba Miele, Gianni Virgili, Stanislao Rizzo

Abstract


Brown syndrome is a rare mechanical disorder characterized by restriction of the superior oblique trochlea-tendon complex.  Marcus-Gunn jaw winking ptosis is a more common congenital oculofacial synkinesis in which blepharoptosis is associated with upper eyelid contraction that accompanies jaw movement.  In this report, we present the case of a 50-year-old woman with unilateral Brown syndrome and Marcus-Gunn jaw winking ptosis in the fellow eye.


Keywords


Brown syndrome; superior oblique tendon; trochlea; Marcus-Gunn; jaw winking ptosis; blepharoptosis; aberrant innervation

References


Wilson ME, Eustis HS Jr, Parks MM. Brown's syndrome. Surv Ophthalmol. 1989; 34(3): 153-72.

Gunn RM. Congenital ptosis with peculiar associated movements of the affected lid. Trans Ophthal Soc UK. 1883; 3: 283-7.

Disorders of the eyelids. In: Kanski JJ, ed. Clinical Ophthalmology, 3rd ed. Butterworth-Heinemann Medical; 1997, p. 1-26.

Torres MR, Calixto N Jr, Oliveira LR, et al. Marcus-Gunn Phenomenon: differential diagnosis of palpebral ptoses in children. J Pediatr (Rio J). 2004 May-Jun;80(3):249-52.

Sundareswaran S, Nipun CA, Kumar V. Jaw - winking phenomenon: Report of a case with review of literature. Indian J Dent Res. 2015; 26(3): 320-3.

Pratt SP, Beyer CK, Johnson CC. The Marcus-Gunn phenomenon. Ophthalmology. 1984; 91: 27-30.

Brodsky MC, Pollock SC, Buckley EG. Neural misdirection in congenital ocular fibrosis syndrome: implications and pathogenesis. J Pediatr Ophtalmol Strabismus. 1989; 26(4): 159-61.

Isenberg S, Blechman B. Marcus-Gunn jaw winking and Duane's retraction syndrome. J Pediatr Ophthalmol Strabismus. 1983; 20(6): 235-7.

Szretter K, Wójtowicz S. An atypical case of unilateral Brown's syndrome with coexisting abortive Marcus-Gunn synkinetic movements. Klin Oczna. 1968; 38(2): 405-9.

Artifoni E, Bertoncini G. On a rare familial association of the Brown syndrome with the Marcus-Gunn phenomenon. Ann Ottalmol Clin Ocul. 1965; 91(7): 563-76.




DOI: http://dx.doi.org/10.16964/er.v4i1.81

Refbacks

  • There are currently no refbacks.




Creative Commons License
This work is licensed under a Creative Commons Attribution 3.0 License.

Eye Reports [eISSN 2039-4756] is a new Open Access, online-only, peer-reviewed journal.